Abstract:
Kaposiform hemangioendothelioma is a rare vascular tumor and has a high mortality
rate in newborns when associated with Kasabach-Merritt syndrome. We present a case of
a newborn with a huge lower limb Kaposiform hemangioendothelioma with a rapid tumor
growth and a life-threatening Kasabach-Merritt syndrome, which was refractory to medical
treatment.