Abstract:
Chordoma, lesion derived from the notochord, represents about 4% of the primary
malignant bone tumours. Males are affected more commonly than females and it is very rare
in children;the peak incidence is in the sixth decade of life.The sacrococcygeal region
accounts for 50% of cases and the spheno-occipital region or the base of the skull for 37% of
cases.The remainder of the cases reported occur in the descending order of frequency in the
cervical,thoracic and the lumbar spine.It is found to be rarely involving the lumbar
spine(about 2%).We present a case of chordoma involving L4 and L5 vertebral body and
disc.The role of epithelial cell marker study has proved a well adjunct to the histopathological
diagnosis of chordoma.